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Transcript

PANCYTOPENIA

RISK FACTORS

ENVIRONMENTAL CAUSES

CAUSES

  • CHEMOTHERAPY
  • EXPOSURE TO ENVIRONMENTAL TOXINS (BENZENE AND ARSENIC)
  • FAMILY HISTORY OF BLOOD DISORDERS
  • LUPOS OR OTHER CERTAIN AUTOIMMUNE DISORDERS
  • PREGNANCY
  • RADIATION EXPOSURE

QUESTIONS

  • CERTAIN MEDICATION INCLUDING SOME ANITBIOTICS AND IMMUNOSUPPRESSANT DRUGS
  • CHEMICAL TOXINS SUCH AS BENZENE
  • CHEMOTHERAPHY
  • RADIATION EXPOSURE
  • VIRAL INFECTIONS

WHAT IS ONE TREATMENT FOR SEVERE CASES OF PANCYTOPENIA?

WHAT IS ONE TYPE OF ENVIRONMENTAL CAUSES FOR PANCYTOPENIA?

  • HEREDITY
  • MEDICATIONS
  • EXPOSURE TO ENVRIONMENTAL CONTAMINATION (I.E RADIATION OR ARSENIC)
  • IN IDIOPATHIC CASES, THE EXACT CAUSE IS UNKNOWN

MEDICATIONS

WHAT IS ONE TYPE OF PANCYTOPENIA?

TREATMENTS

SERIOUS SYMPTOMS

TRUE OR FALSE: OLDER PATIENTS ARE MORE LIKELY TO GET BETTER AFTER TREATMENT?

  • ANTITHYMOCYTE ANTIBODIES (THYMOGLOBULIN), WHICH SUPPRESS THE BODY'S NATURAL IMMUNE RESPONSE
  • CORTICOSTEROIDS SUCH AS METHYLPREDNISOLONE
  • CYCLOPHOSPHAMIDE (CYTOXAN)
  • CYCLOSPORINE(SANDIMMUNE, NEORAL)
  • IN VERY MILD CASES,
  • TREATMENT MAY NOT BE NECESSARY
  • MODERATE CASES
  • BLOOD TRANFUSION MAY HELP RESTORE BOOD CELLS COUNT
  • SEVERE CASES
  • BONE MARROW TRANSPLANT
  • STEM CELL THERAPY MAY BE REQUIRED TO RESTORE THE ABILITY OF BONE MARROW TO PRODUCE BLOOD CELLS

SYMPTOMS

  • CONFUSION OR LOSS OF CONSCIOUSNESS FOR EVEN A BRIEF MOMENT
  • EXCESSIVE FATIGUE, WEAKNESS, OR SHORTNESS OF BREATH
  • HIGH FEVER(+101F)

RESULTS

  • MORE EFFECTIVE IN YOUNGER PATIENTS
  • OLDER PATIENTS MAY REQUIRE THE USE OF IMMUNOSUPPRESSANT DRUGS

POTENTIAL COMPLICATIONS

  • BLEEDING IN THE BRAIN
  • COMPLICATIONS FROM BLOOD TRANFUSIONS
  • COMPLICATIONS FROM MEDICATIONS
  • POOR REACTION TO BONE MARROW TRANSPLANT
  • SEPSIS(LIFE-THREATENING BACTERIAL BLOOD INFECTION)
  • SEVERE BLEEDING
  • INCLUDE GENERALIZE SYMPTOMS SUCH AS FATIGUE AND WEAKNESS
  • SKIN SYMPTOMS
  • EASY BRUSING
  • RASH
  • BLEEDING
  • NOSEBLEEDS
  • BLEEDING OF THE GUMS
  • UNEXPLAINED BLEEDING
  • BLEEDING IN THE INTERNAL ORGANS

WHAT IS PANCYTOPENIA

  • A DEFICIENCY OF ALL TYPES OF BLOOD CELLS INCLUDING WHITE BLOOD CELLS, RED BLOOD CELLS, AND PLATELETS
  • IT OCCURS WHEN YOUR BODY CANNOT PRODUCE ENOUGH BLOOD CELLS BECAUSE THE BONE MARROW STEM CELLS THAT FORM BLOOD CELLS DO NOT FUNCTION NORMALLY

TWO FORMS

  • IDIOPATHIC, IN WHICH THE CAUSE IS NOT KNOWN, BUT IS OFTEN AUTOIMMUNE, MEANING THAT THE BODY ATTACKS ITS OWN TISSUES AS FOREIGN SUBSTANCES
  • OFTEN CAUSED BY ENVIRONMENTAL FACTORS

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